Kraniofasiyal Tutulum Gösteren Poliostatik Fibröz Displazi: Olgu Sunumu

Elif Kaya

doi:10.7126/cdj.58140.1008002461

EN TR

Kraniofasiyal Tutulum Gösteren Poliostatik Fibröz Displazi: Olgu Sunumu

Öz

Fibröz displazi kemiğin, nedeni bilinmeyen, kanselöz kemiğin tüm bileşenlerinin yerini, farklı oranda anormal görünümlü kemik içeren fibröz dokunun almasıyla sonuçlanan iskelet lezyonudur. Klinik olarak üç farklı tipi vardır; monostatik tip, tek bir kemiği etkiler ve tüm vakaların % 70 ini oluşturur. Poliostatik tip birden fazla kemiği etkiler ve % 20-30 oranında görülür. McCune-Albright sendromu (MAS) ise endokrin bozukluğu ile karakterize fibröz displazinin diğer bir formudur. Radyografik olarak fibröz displazi lezyonlarının periferleri genellikle belirsizdir ve kemiğin internal yapısı, daha radyolüsent, daha radyoopak ya da bu ikisinin bir karışımı şeklinde görülebilir. Bu olgu sunumunda kranial ve vertebral tutulumu olan poliostatik fibröz displazi hastalığına sahip 25 yaşında kadın hastanın klinik ve radyografik bulguları değerlendirilerek literatürdeki olgularla karşılaştırılarak tartışılacaktır.

Anahtar Kelimeler

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Details

Primary Language

Turkish

Subjects

Health Care Administration

Journal Section

Research Article

Authors

Elif Kaya

Publication Date

February 11, 2015

Submission Date

November 7, 2013

Acceptance Date

-

Published in Issue

Year 2015 Volume: 18 Number: 1

DOI

https://doi.org/10.7126/cdj.58140.1008002461

IZ

https://izlik.org/JA42MA36DZ

Cite

RIS / Bibtex

EndNote

Kaya E (February 1, 2015) Kraniofasiyal Tutulum Gösteren Poliostatik Fibröz Displazi: Olgu Sunumu. Cumhuriyet Dental Journal 18 1 71–78.

Kraniofasiyal Tutulum Gösteren Poliostatik Fibröz Displazi: Olgu Sunumu

Polyostotic fibrous dysplasia with craniofacial involvement

Abstract

Keywords

Kraniofasiyal Tutulum Gösteren Poliostatik Fibröz Displazi: Olgu Sunumu

Öz

Anahtar Kelimeler

References

Details

Primary Language

Subjects

Journal Section

Authors

Publication Date

Submission Date

Acceptance Date

Published in Issue

DOI

IZ

Cite