Glukoz 6 fosfat dehidrogenaz eksikliği olan pediatrik hastada anestezi yönetimi

Sedef Gülçin Ural; Meltem Aktay İnan

doi:10.17826/cutf.323982

Olgu Sunumu

Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency

Yıl 2017, Cilt: 42 Sayı: 3, 552 - 555, 30.09.2017

Sedef Gülçin Ural Meltem Aktay İnan

https://doi.org/10.17826/cutf.323982

Öz

Glucose 6 phospate dehydrogenase (G6PD) deficiency is the most common enzyme deficiency. It is inherited in an X-linked recessive pattern and cause some disorders like hyperbilirubinemia in newborns, acut and chronic hemolysis. The first and main goal of the anethesia in this patient is to prevent oxidative stress. In this case we aim to share applying general anesthesia safely in patients with G6PD deficiency

Anahtar Kelimeler

Glucose 6 phospate dehydrogenase deficiency, anesthesia management, pediatric patient.

Kaynakça

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