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PARRY ROMBERG SENDROMLU PEDİATRİK BİR HASTANIN NADİR ORAL BULGULARI: BİR OLGU SUNUMU

Yıl 2024, Cilt: 13 Sayı: 1, 155 - 160, 26.01.2024

Derya Sarıoğlu Özge Anıl

https://doi.org/10.54617/adoklinikbilimler.1284842

Öz

Skleroderma; kollajen yapım ve yıkımında ortaya çıkan bozukluklardan kaynaklanan, deri ve deri altı dokularda kalınlaşmaya ve sertleşmeye yol açan kronik bir hastalıktır. Pek çok alt tipi olan sklerodermanın çocuklarda en çok görülen tipi; lokalize sklerodermanın lineer formu, diğer bir deyişle morfeadır. Morfea; çene bölgesini etkilediği zaman, iskeletsel ve dişsel ortodontik malformasyonlara ve dişlerde sürme gecikmelerine neden olabilmektedir. Morfeanın; deri, deri altı dokulara ve kemiğe kadar ilerleyebilen progresif hemifasial atrofiyle seyreden formuna Parry Romberg Sendromu adı verilir. Parry Romberg sendromu nörokutanoz bir rahatsızlıktır. Bu vaka sunumunda, Parry Romberg Sendromu’na sahip pediatrik bir hastada görülen, nadir ekstraoral ve intraoral bulgulardan bahsedilmiştir.

Anahtar Kelimeler

lokalize skleroderma morfea pedodonti

Destekleyen Kurum

-

Proje Numarası

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Teşekkür

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Kaynakça

  • Referans1. Fett N, Werth VP. Update on morphea: part I. Epidemiology, clinical presentation, and pathogenesis. J Am Acad Dermatol 2011;64:217–28.
  • Referans2. Weibel L, Sampaio MC, Visentin MT, Howell KJ, Woo P, Harper JI. Evaluation of methotrexate and corticosteroids for the treatment of localized scleroderma (morphoea) in children. Br J Dermatol 2006;155:1013–20.
  • Referans3. Bhoyrul B, Clark S. Parry-Romberg syndrome and morphoea en coup de sabre. Arch Dis Child 2019;104:400.
  • Referans4. Misra R, Singh G, Aggarwal P, Aggarwal A. Juvenile onset systemic sclerosis: a single center experience of 23 cases from Asia. Clin Rheumatol 2007;26:1259–62.
  • Referans5. Foeldvari I. Scleroderma in children. Curr Opin Rheumatol 2002;14:699–703.
  • Referans6. Ullman S, Danielsen PL, Fledelius HC, Daugaard-Jensen J, Serup J. Scleroderma en Coup de Sabre, Parry-romberg hemifacial atrophy and associated manifestations of the eye, the oral cavity and the teeth: a Danish follow-up study of 35 patients diagnosed between 1975 and 2015. Dermatology 2021;237:204– 12.
  • Referans7. Sevimli İ, Öztürk P, Mülayım MK, Nazik H, Geç Başlangıçlı Lineer Skleroderma. Turkish J Fam Med Prim Care 12:153–5.
  • Referans8. Holland KE, Steffes B, Nocton JJ, Schwabe MJ, Jacobson RD, Drolet BA. Linear scleroderma en coup de sabre with associated neurologic abnormalities. Pediatrics 2006;117:e132–6.
  • Referans9. Wong M, Phillips CD, Hagiwara M, Shatzkes DR. Parry Romberg syndrome: 7 cases and literature review. Am J Neuroradiol 2015;36:1355–61.
  • Referans10. Anderson LE, Treat JR, Licht DJ, Kreiger PA, Knight AM. Remission of seizures with immunosuppressive therapy in Parry- Romberg syndrome and en coup de sabre linear scleroderma: Case report and brief review of the literature. Pediatr Dermatol 2018;35:e363–5.
  • Referans11. Yim S, Yang I-H, Baek S-H. Characterization of dental phenotypes and treatment modalities in Korean patients with Parry-Romberg syndrome. Korean J Orthod 2020;50:407–17.
  • Referans12. Cui Y, Zhao J, Hu X, Fang B, Mao L. Combined Surgical- Orthodontic Treatment of Patients With Severe Parry-Romberg Syndrome. J Craniofac Surg 2022;33:e564–9.
  • Referans13. Kumar NG, Maurya BS, Sudeep CS. Parry Romberg syndrome: literature review and report of three cases. J Maxillofac Oral Surg 2019;18:210–6.
  • Referans14. Salimov F, Barış Ş, Dalili M, Koçak EF. Diş Mobilitesi ve İmplant Stabilitesi için Kullanılan Ölçüm Yöntemleri. Arşiv Kaynak Tarama Derg 2019;28:130–9.
  • Referans15. Van der Cruyssen F, Meeus J, Schoenaers J, Politis C. Parry Romberg syndrome: A long-term retrospective cohort study of 10 patients. Oral Maxillofac Surg Cases 2018;4:73–83.
  • Referans16. Arif T, Majid I, Haji MLI. Late onset ‘en coup de sabre’following trauma: Rare presentation of a rare disease. Our Dermatology Online 2015;6:49.
  • Referans17. Brownell I, Soter NA. Familial linear scleroderma (en coup de sabre) responsive to antimalarials and narrowband ultraviolet B therapy. Dermatol Online J 2007;13.
  • Referans18. Zulian F, Athreya BH, Laxer R, Nelson AM, Feitosa de Oliveira SK, Punaro MG, et al. Juvenile localized scleroderma: clinical and epidemiological features in 750 children. An international study. Rheumatology 2006;45:614–20.
  • Referans19. Müller L, van Waes H, Langerweger C, Molinari L, Saurenmann RK. Maximal mouth opening capacity: percentiles for healthy children 4–17 years of age. Pediatr Rheumatol 2013;11:1–7.
  • Referans20. Hørberg M, Lauesen SR, Daugaard-Jensen J, Kjær I. Linear scleroderma en coup de sabre including abnormal dental development. Eur Arch Paediatr Dent 2015;16:227–31.

RARE ORAL FINDINGS OF A PEDIATRIC PATIENT WITH PARRY ROMBERG SYNDROME: A CASE REPORT

Yıl 2024, Cilt: 13 Sayı: 1, 155 - 160, 26.01.2024

Derya Sarıoğlu Özge Anıl

https://doi.org/10.54617/adoklinikbilimler.1284842

Öz

Scleroderma is a chronic disease that causes thickening and hardening of the skin and subcutaneous tissues, resulting from disorders in collagen production and destruction. The most common type of scleroderma in children, which has many subtypes; is the linear form of localized scleroderma, in other words, morphea. Morphea; When it affects the jaw area, it can cause skeletal and dental orthodontic malformations and tooth eruption delays. Morphea; The form with progressive hemifacial atrophy that can progress to the skin, subcutaneous tissues and bone is called Parry Romberg Syndrome. Parry Romberg syndrome is a neurocutaneous disorder. In this case report, rare extraoral and intraoral findings in a pediatric patient with Parry Romberg Syndrome are discussed.

Anahtar Kelimeler

localized scleroderma morphea pedodontics

Proje Numarası

-

Kaynakça

  • Referans1. Fett N, Werth VP. Update on morphea: part I. Epidemiology, clinical presentation, and pathogenesis. J Am Acad Dermatol 2011;64:217–28.
  • Referans2. Weibel L, Sampaio MC, Visentin MT, Howell KJ, Woo P, Harper JI. Evaluation of methotrexate and corticosteroids for the treatment of localized scleroderma (morphoea) in children. Br J Dermatol 2006;155:1013–20.
  • Referans3. Bhoyrul B, Clark S. Parry-Romberg syndrome and morphoea en coup de sabre. Arch Dis Child 2019;104:400.
  • Referans4. Misra R, Singh G, Aggarwal P, Aggarwal A. Juvenile onset systemic sclerosis: a single center experience of 23 cases from Asia. Clin Rheumatol 2007;26:1259–62.
  • Referans5. Foeldvari I. Scleroderma in children. Curr Opin Rheumatol 2002;14:699–703.
  • Referans6. Ullman S, Danielsen PL, Fledelius HC, Daugaard-Jensen J, Serup J. Scleroderma en Coup de Sabre, Parry-romberg hemifacial atrophy and associated manifestations of the eye, the oral cavity and the teeth: a Danish follow-up study of 35 patients diagnosed between 1975 and 2015. Dermatology 2021;237:204– 12.
  • Referans7. Sevimli İ, Öztürk P, Mülayım MK, Nazik H, Geç Başlangıçlı Lineer Skleroderma. Turkish J Fam Med Prim Care 12:153–5.
  • Referans8. Holland KE, Steffes B, Nocton JJ, Schwabe MJ, Jacobson RD, Drolet BA. Linear scleroderma en coup de sabre with associated neurologic abnormalities. Pediatrics 2006;117:e132–6.
  • Referans9. Wong M, Phillips CD, Hagiwara M, Shatzkes DR. Parry Romberg syndrome: 7 cases and literature review. Am J Neuroradiol 2015;36:1355–61.
  • Referans10. Anderson LE, Treat JR, Licht DJ, Kreiger PA, Knight AM. Remission of seizures with immunosuppressive therapy in Parry- Romberg syndrome and en coup de sabre linear scleroderma: Case report and brief review of the literature. Pediatr Dermatol 2018;35:e363–5.
  • Referans11. Yim S, Yang I-H, Baek S-H. Characterization of dental phenotypes and treatment modalities in Korean patients with Parry-Romberg syndrome. Korean J Orthod 2020;50:407–17.
  • Referans12. Cui Y, Zhao J, Hu X, Fang B, Mao L. Combined Surgical- Orthodontic Treatment of Patients With Severe Parry-Romberg Syndrome. J Craniofac Surg 2022;33:e564–9.
  • Referans13. Kumar NG, Maurya BS, Sudeep CS. Parry Romberg syndrome: literature review and report of three cases. J Maxillofac Oral Surg 2019;18:210–6.
  • Referans14. Salimov F, Barış Ş, Dalili M, Koçak EF. Diş Mobilitesi ve İmplant Stabilitesi için Kullanılan Ölçüm Yöntemleri. Arşiv Kaynak Tarama Derg 2019;28:130–9.
  • Referans15. Van der Cruyssen F, Meeus J, Schoenaers J, Politis C. Parry Romberg syndrome: A long-term retrospective cohort study of 10 patients. Oral Maxillofac Surg Cases 2018;4:73–83.
  • Referans16. Arif T, Majid I, Haji MLI. Late onset ‘en coup de sabre’following trauma: Rare presentation of a rare disease. Our Dermatology Online 2015;6:49.
  • Referans17. Brownell I, Soter NA. Familial linear scleroderma (en coup de sabre) responsive to antimalarials and narrowband ultraviolet B therapy. Dermatol Online J 2007;13.
  • Referans18. Zulian F, Athreya BH, Laxer R, Nelson AM, Feitosa de Oliveira SK, Punaro MG, et al. Juvenile localized scleroderma: clinical and epidemiological features in 750 children. An international study. Rheumatology 2006;45:614–20.
  • Referans19. Müller L, van Waes H, Langerweger C, Molinari L, Saurenmann RK. Maximal mouth opening capacity: percentiles for healthy children 4–17 years of age. Pediatr Rheumatol 2013;11:1–7.
  • Referans20. Hørberg M, Lauesen SR, Daugaard-Jensen J, Kjær I. Linear scleroderma en coup de sabre including abnormal dental development. Eur Arch Paediatr Dent 2015;16:227–31.
Toplam 20 adet kaynakça vardır.

Ayrıntılar

Birincil Dil Türkçe
Konular Diş Hekimliği
Bölüm Olgu Sunumu
Yazarlar

Derya Sarıoğlu 0009-0004-1905-3230

Özge Anıl 0000-0003-0092-2315

Proje Numarası -
Yayımlanma Tarihi 26 Ocak 2024
Gönderilme Tarihi 19 Nisan 2023
Yayımlandığı Sayı Yıl 2024 Cilt: 13 Sayı: 1

Kaynak Göster

Vancouver Sarıoğlu D, Anıl Ö. PARRY ROMBERG SENDROMLU PEDİATRİK BİR HASTANIN NADİR ORAL BULGULARI: BİR OLGU SUNUMU. ADO Klinik Bilimler Dergisi. 2024;13(1):155-60.
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